European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis.
نویسندگان
چکیده
Patients with LAM usually develop progressive dyspnoea and recurrent pneumothorax, chylous collections and occasional haemoptysis [1]. Extra pulmonary lymphadenopathy and cystic masses of the axial lymphatics termed lymphangioleiomyomas can result in abdominal and pelvic lymphatic obstruction [7]. LAM is often associated with angiomyolipoma in the kidneys [8], and an increased frequency of meningioma [9]. LAM varies in clinical features and rate of progression: this together with an absence of clear prognostic factors results in patients being given conflicting information about prognosis.
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عنوان ژورنال:
- The European respiratory journal
دوره 35 1 شماره
صفحات -
تاریخ انتشار 2010